PT  - JOURNAL ARTICLE
AU  - Santavy, Petr
TI  - Multidisciplinary approach to a Marfan syndrome patient with emphasis on cardiovascular complications
DP  - 2013 Mar 1
TA  - Biomedical papers
PG  - 1--4
VI  - 157
IP  - 1
AID - 10.5507/bp.2013.023
IS  - 12138118
AB  - Background: Marfan syndrome (MFS) is the most common inherited disorder of connective tissue affecting multiple organ systems. The most life-threatening and life-shortening complication is aortic dissection. Without surgery, life expectancy of MFS patients is reduced to approximately 32 years. Early identification and appropriate multidisciplinary medical cooperation is essential.
Conclusion: Proper follow up, therapy and timely surgical repair lead to an almost normal lifespan in affected individuals.