PT Journal
AU Santavy, P
TI Multidisciplinary approach to a Marfan syndrome patient with emphasis on cardiovascular complications
SO Biomedical papers
PY 2013
BP 1
EP 4
VL 157
IS 1
DI 10.5507/bp.2013.023
DE Marfan syndrome; aneurysms; aorta; aortic dissection; cardiovascular complications
AB Background: Marfan syndrome (MFS) is the most common inherited disorder of connective tissue affecting multiple organ systems. The most life-threatening and life-shortening complication is aortic dissection. Without surgery, life expectancy of MFS patients is reduced to approximately 32 years. Early identification and appropriate multidisciplinary medical cooperation is essential.Conclusion: Proper follow up, therapy and timely surgical repair lead to an almost normal lifespan in affected individuals.
ER