Biomedical papers, 2013 (vol. 157), issue 1

Biomed Pap Med Fac Univ Palacky Olomouc Czech Repub. 2013, 157(1):1-4 | 10.5507/bp.2013.023

Multidisciplinary approach to a Marfan syndrome patient with emphasis on cardiovascular complications

Petr Santavy
Department of Cardiac Surgery, University Hospital Olomouc, Czech Republic

Background: Marfan syndrome (MFS) is the most common inherited disorder of connective tissue affecting multiple organ systems. The most life-threatening and life-shortening complication is aortic dissection. Without surgery, life expectancy of MFS patients is reduced to approximately 32 years. Early identification and appropriate multidisciplinary medical cooperation is essential.

Conclusion: Proper follow up, therapy and timely surgical repair lead to an almost normal lifespan in affected individuals.

Keywords: Marfan syndrome, aneurysms, aorta, aortic dissection, cardiovascular complications

Received: March 6, 2013; Accepted: March 22, 2013; Published: March 25, 2013; Published: March 1, 2013


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